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Cardiac tumours in children: a single-centre experience and literature review

Part of: Basic Science

Published online by Cambridge University Press:  28 February 2022

Diogo Faim Open the ORCID record for Diogo Faim [Opens in a new window] ,
Andreia Francisco Open the ORCID record for Andreia Francisco [Opens in a new window]  and
António Pires
Diogo Faim*
Affiliation:
Department of Paediatric Cardiology, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
Andreia Francisco
Affiliation:
Department of Paediatric Cardiology, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
António Pires
Affiliation:
Department of Paediatric Cardiology, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal
*
Author for correspondence: D. Faim, Department of Paediatric Cardiology, Centro Hospitalar e Universitário de Coimbra, Avenida Dr. Afonso Romão, Coimbra 3000-602, Portugal. Tel: +351967768038; Fax: 239 717 216. E-mail: diogofaim92@gmail.com
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Abstract

Cardiac tumours are extremely rare in children. Although more than 90% are benign, children can develop obstructive or embolisation derived symptoms, arrhythmias, constitutional symptoms, cardiac tamponade, or even sudden death. Although the majority are asymptomatic, and some spontaneously regress, appropriate follow-up is needed on a case-by-case basis, as patients may develop late symptoms. Definitive diagnosis is only possible through histological analysis; however, it is possible to infer tumour type with a high grade of certainty based on imaging features, particularly cardiac magnetic resonance. Surgical resection is advocated for those causing symptoms, obstruction, cardiac dysfunction, and high risk of embolisation. The aim of this review is to present the state of the art related to cardiac tumours in the paediatric population, in the context of our own experience.

Keywords

Cardiac tumourheart tumourchildrenpaediatricspaediatric cardiology
Type
Review
Information
Cardiology in the Young , Volume 32 , Issue 3 , March 2022 , pp. 347 - 356
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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