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The diagnostic evaluation of patients with complete transposition

Published online by Cambridge University Press:  19 August 2008

Michael L. Rigby*
Affiliation:
Department of Paediatrics, National Heart & Lung Institute, Royal Brompton and National Heart Hospital, London, and the Department of Pediatrics, National University Hospital, Kent Ridge, Singapore
Kit-Yee Chan
Affiliation:
Department of Paediatrics, National Heart & Lung Institute, Royal Brompton and National Heart Hospital, London, and the Department of Pediatrics, National University Hospital, Kent Ridge, Singapore
*
Dr. Michael L. Rigby Department of Paediatrics, Royal Brompton and National Heart Hospital, Fulham Road, LondonSW3 6HP, United Kingdom

Summary

The vast majority of patients with complete transposition present during either the neonatal period or early infancy. Almost always the diagnosis and the categorization of associated lesions can be established by cross-sectional echocardiography. Doppler techniques usually provide enough information about flows to allow palliative or radical surgery to be undertaken without formal cardiac catheterization, because balloon atrial septostomy is carried out with echocardiographic imaging, often on the intensive care unit. Angiography is occasionally performed to visualize the pulmonary arteries or the aorta, and, if there is suspicion of a significant elevation of the pulmonary vascular resistance, it must be measured at cardiac catheterization. Neither cross-sectional echocardiography nor aortography is entirely reliable in identifying those patterns of the coronary arteries which are a contraindication to the arterial switch operation. There is, as yet, no evidence that either magnetic resonance imaging or transesophageal echocardiography are superior to more conventional methods of preoperative diagnosis in complete transposition and it seems unlikely that they will be required.

Type
Original Articles
Copyright
Copyright © Cambridge University Press 1991

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