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A fatal case of idiopathic restrictive cardiomyopathy

Published online by Cambridge University Press:  24 May 2005

Przemysław Palka ,
Aleksandra Lange  and
Cameron Ward
Przemysław Palka
Affiliation:
St Andrew's Heart Institute & Department of Echocardiography, Prince Charles Hospital Queensland, Australia
Aleksandra Lange
Affiliation:
Department of Pediatric Cardiology Children Mater Hospital, Brisbane, Queensland, Australia
Cameron Ward
Affiliation:
St Andrew's Heart Institute & Department of Echocardiography, Prince Charles Hospital Queensland, Australia
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Abstract

We describe the clinical features of idiopathic restrictive cardiomyopathy in a female infant. A marked elevation of left ventricular end-diastolic pressure, and profoundly abnormal myocardial relaxation, were detected with the use of Doppler blood flow echocardiography, coupled with the relatively new technique of Doppler tissue echocardiography. There was no clinical evidence of ongoing heart failure, but she had signs of myocardial ischaemia, and unfortunately died suddenly at the age of 13 months.

Keywords

Childhood restrictive cardiomyopathydiastolic dysfunctionDoppler tissue echocardiography
Type
Brief Report
Information
Cardiology in the Young , Volume 13 , Issue 5 , October 2003 , pp. 469 - 471
Copyright
© 2003 Cambridge University Press

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