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Heart transplant after the Fontan operation

Published online by Cambridge University Press:  09 January 2014

Joseph W. Rossano  and
Robert E. Shaddy
Joseph W. Rossano
Affiliation:
Department of Pediatrics, Perelman School of Medicine, The Cardiac Center, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Robert E. Shaddy*
Affiliation:
Department of Pediatrics, Perelman School of Medicine, The Cardiac Center, The Children's Hospital of Philadelphia, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: R. E. Shaddy, MD, The Children's Hospital of Philadelphia, Division of Cardiology, 34th Street and Civic Center Boulevard, Room 8NW80, Philadelphia, PA 19104, United States of America. Tel: 267-426-7518; Fax: 267-426-0950; E-mail: shaddyr@email.chop.edu
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Abstract

Although the Fontan operation may provide a durable circulation for some patients with functionally univentricular hearts for several decades, circulatory failure becomes more common over time. Medical and/or surgical interventions can improve the circulation for some period of time; however, many patients will experience end-stage circulatory failure. Heart transplantation may be considered in these patients. This review will cover the indications and evaluation for heart transplantation, management of patients while waiting for heart transplantation and the current outcomes of transplantation in this population.

Keywords

Fontanheart transplantheart failure
Type
Original Article
Information
Cardiology in the Young , Volume 23 , Issue 6: HeartWeek 2013 , December 2013 , pp. 841 - 846
Copyright
Copyright © Cambridge University Press 2013 

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