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Staged surgical management of pulmonary atresia with intact ventricular septum

Published online by Cambridge University Press:  19 August 2008

Sergio A. Battistessa ,
Mark Jackson ,
David I. Hamilton ,
Raman G. Patel  and
Roxane McKay
Sergio A. Battistessa
Affiliation:
From the Cardiac Units, Royal Liverpool and Manchester Children's Hospitals and the Institute of Child Health, University of Liverpool, Liverpool
Mark Jackson
Affiliation:
From the Cardiac Units, Royal Liverpool and Manchester Children's Hospitals and the Institute of Child Health, University of Liverpool, Liverpool
David I. Hamilton
Affiliation:
From the Cardiac Units, Royal Liverpool and Manchester Children's Hospitals and the Institute of Child Health, University of Liverpool, Liverpool
Raman G. Patel
Affiliation:
From the Cardiac Units, Royal Liverpool and Manchester Children's Hospitals and the Institute of Child Health, University of Liverpool, Liverpool
Roxane McKay*
Affiliation:
From the Cardiac Units, Royal Liverpool and Manchester Children's Hospitals and the Institute of Child Health, University of Liverpool, Liverpool
*
Dr.Roxane McKay, Cardiac Unit, Royal Liverpool Children's Hospital, Eaton Road, Liverpool L12 2AP, United Kingdom. Tel. 51-228-4811 Extension 2635; Fax. 51-228-0328.
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Abstract

Review of an institutional experience of 81 patients admitted to the Royal Liverpool Children's Hospital between January 1958 and December 1990 with a diagnosis of pulmonary atresia and intact ventricular septum revealed that successful definitive repair was achieved in about one-third of those who underwent surgical treatment. A three-stage protocol, consisting of a systemic-pulmonary anastomosis followed by right ventricular decompression on cardiopulmonary bypass and subsequent separation of the systemic and pulmonary circulations, facilitated a biventricular correction but rarely led to a successful Fontan procedure. Both functional class and probability of survival improved after each stage of management.

Keywords

pulmonary atresiahypoplastic right heart
Type
World Forum for Pediatric Cardiology Symposium on Pulmonary Atresia
Information
Cardiology in the Young , Volume 2 , Issue 4 , October 1992 , pp. 395 - 402
Copyright
Copyright © Cambridge University Press 1992

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