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Total anomalous systemic venous drainage in left heterotaxy syndrome

Published online by Cambridge University Press:  28 May 2012

Ravindranath S. Khandenahally ,
Surender Deora  and
Ravi S. Math
Ravindranath S. Khandenahally
Affiliation:
Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Rajiv Gandhi University of Health Sciences, Bangalore-69, Karnataka, India
Surender Deora*
Affiliation:
Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Rajiv Gandhi University of Health Sciences, Bangalore-69, Karnataka, India
Ravi S. Math
Affiliation:
Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Rajiv Gandhi University of Health Sciences, Bangalore-69, Karnataka, India
*
Correspondence to: Dr S. Deora, MD, DM, B-3/14, Goyal Intercity, Near SAL Hospital, Thaltej, Ahmedabad, Gujarat 380054, India. Tel: +91 8238422947; Fax: +91 7926407711; E-mail: drsdeora@indiatimes.com
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Abstract

Total anomalous systemic venous drainage is an extremely rare congenital heart defect. In this study we describe an 11-year-old girl who presented with a history of fatigue and central cyanosis that she had had since early childhood with unremarkable precordial examination results. Investigations revealed left heterotaxy with all systemic venous drainage to the left-sided atrium with non-compaction of the left ventricle.

Keywords

Cyanosissystemic venous anomalynon-compaction
Type
Brief Report
Information
Cardiology in the Young , Volume 23 , Issue 2 , April 2013 , pp. 284 - 286
Copyright
Copyright © Cambridge University Press 2012 

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References

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