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An Atypical Case of Progressive Supranuclear Palsy

Published online by Cambridge University Press:  18 September 2015

Andrew J. Gomori  and
Anders A.F. Sima
Andrew J. Gomori
Affiliation:
Sections of Neurology, Department of Medicine and Neuropathology, University of Manitoba and Health Sciences Centre, Winnipeg, Manitoba
Anders A.F. Sima
Affiliation:
Department of Pathology, University of Manitoba and Health Sciences Centre, Winnipeg, Manitoba
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Summary

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We report a 59 year old woman who presented with double vision, nuchal pain and mild dementia. On neurological examination she demonstrated third, sixth and seventh nerve palsies and ataxia. Following intravenous ACTH and oral prednisone therapy she showed a remarkable recovery which left her with only a left facial weakness. She remained well for two years. She then developed bulbar palsy and profound dementia. Pathological examination revealed progressive supranuclear palsy (PSP). This patient demonstrated a greater variability in the course of PSP than has previously been recognized.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 11 , Issue 1 , February 1984 , pp. 48 - 52
Copyright
Copyright © Canadian Neurological Sciences Federation 1984

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