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Cardiac Angiographic Findings in Friedreich's Ataxia

Published online by Cambridge University Press:  18 September 2015

R. Guerin ,
G. Elias ,
A. Davignon ,
M. Cote ,
G. Geoffroy ,
B. Lemieux  and
A. Barbeau
R. Guerin
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
G. Elias
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
A. Davignon
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
M. Cote
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
G. Geoffroy
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
B. Lemieux
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
A. Barbeau*
Affiliation:
Hôpital Ste-Justine, Montreal; the Hôpital Maisonneuve-Rosemont, Montreal; the Centre Hospitaller de l'Université de Sherbrooke; and the Clinical Research Institute of Montreal
*
Clinical Research Institute of Montreal, 110 Pine Avenue West, Montreal, H2W IR7 Quebec, Canada
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Summary:

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Angiograms of 12 patients with typical Friedreich's ataxia were analyzed. The results corroborate previous reports and justify the conclusion that the cardiomyopathy is of the hypertrophic type. In 10 of 12 cases, the hypertrophy is concentric, and non obstructive. Less frequently (2 cases), this hypertrophy is accompanied by diffuse hypokinesis and depressed ejection fraction.

Type
Quebec Cooperative Study of Friedreich's Ataxia
Information
Canadian Journal of Neurological Sciences , Volume 3 , Issue 4 , November 1976 , pp. 337 - 342
Copyright
Copyright © Canadian Neurological Sciences Federation 1976

References

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