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Visual evoked potentials and brain stem auditory potentials in Friedreich's ataxia — A longitudinal study

Published online by Cambridge University Press:  18 September 2015

J. Bogacz ,
C. Chouza ,
S. Romero ,
A. Bogacz ,
H. Correa  and
A. Barbeau
J. Bogacz
Affiliation:
Laboratorio de Electroencefalographia y Neurofisiologia Clinica
C. Chouza
Affiliation:
The Departamento de Investigacion Clinic
S. Romero
Affiliation:
The Departamento de Investigacion Clinic
A. Bogacz
Affiliation:
Laboratorio de Electroencefalographia y Neurofisiologia Clinica
H. Correa
Affiliation:
The Departamento de Investigacion Clinic
A. Barbeau*
Affiliation:
Instituto de Neurologia, Hospital de Clinicas “Dr. Manuel Quintela”, Montevido Uruguay and the Clinical Research Institute of Montreal
*
Clinical Research Institute of Montreal, 110 Pine Avenue West, Montreal, Quebec, Canada, H2W IR7
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Abstract

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Six patients with Friedreich's ataxia, 4 males and 2 females, their ages ranging from 13 to 33 years, were studied. The early manifestations started between age 7 and 13 with an evolution time between 6 and 20 years. Serial visual and brain stem auditory evoked potential recordings were made. A progressive increase in latency, reduction in amplitude and in latency inter-ocular difference of PlOO were observed. The pattern of the reversal checker-board visual evoked potential was preserved. A disorganized BAEP pattern, a well defined potential I, a very small potential V and a delay in the interpeak latency were constant findings. The assumption is made of a progressive involvement of both visual and central auditory pathways. Pathophysiological mechanisms are discussed.

Type
b—Clinical Physiology and Pathology
Information
Canadian Journal of Neurological Sciences , Volume 11 , Issue S4 , November 1984 , pp. 565 - 569
Copyright
Copyright © Canadian Neurological Sciences Federation 1984

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