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Abnormalities in myocardial perfusion after surgical correction of pulmonary atresia with intact ventricular septum

Published online by Cambridge University Press:  15 January 2008

Britt-Marie Ekman-Joelsson ,
Håkan Berggren ,
Ann-Britt Boll ,
Rune Sixt  and
Jan Sunnegårdh
Britt-Marie Ekman-Joelsson*
Affiliation:
Paediatric and Adolescent Medical Care, Skaraborgs Hospital, Skövde, Sweden
Håkan Berggren
Affiliation:
The Queen Silvia Children’s Hospital, Göteborg University, Göteborg, Sweden
Ann-Britt Boll
Affiliation:
The Queen Silvia Children’s Hospital, Göteborg University, Göteborg, Sweden
Rune Sixt
Affiliation:
The Queen Silvia Children’s Hospital, Göteborg University, Göteborg, Sweden
Jan Sunnegårdh
Affiliation:
The Queen Silvia Children’s Hospital, Göteborg University, Göteborg, Sweden
*
Paediatric and Adolescent Medical Care, Skaraborgs Hospital, 541 85 Skövde, Sweden. Tel: +46-500-431000; Fax: +46-500-432299; E-mail: britt-mari.ekman-joelsson@vgregion.se
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Abstract

We describe the results of myocardial perfusion scintigraphy performed 4 to 15 years after surgery in 12 patients with pulmonary atresia and intact ventricular septum. We used single photon emission computed tomography after injection of technetium Tc-99m tetrofosmin at submaximal exercise test. The patients, 7 girls and 5 boys, with a mean age of 11 years, and a range from 6 to 19 years, had either undergone biventricular repair, in 5 cases, or univentricular palliation in the remaining 7. This second group included 4 patients with ventriculo-coronary arterial communications. Of the children, 3 with biventricular repair and 6 with univentricular palliation had perfusion defects. Children with biventricular repair had perfusion defects in the ventricular septum, while those having univentricular palliation also had defects located to the left ventricular free wall. All children with ventriculo-coronary arterial communications had perfusion defects both in the ventricular septum and in the left ventricular free wall.

Keywords

Myocardial perfusion scintigraphycongenital heart defectFontan circulation
Type
Original Article
Information
Cardiology in the Young , Volume 18 , Issue 1 , February 2008 , pp. 89 - 95
Copyright
Copyright © Cambridge University Press 2008

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