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Arrhythmias in paediatric valvar disease*

Published online by Cambridge University Press:  29 December 2014

Jamie A. Decker
Jamie A. Decker*
Affiliation:
Division of Pediatric Cardiology, All Children’s Heart Institute, Saint Petersburg, Florida, United States of America
*
Correspondence to: J. A. Decker, MD, Division of Pediatric Cardiology, All Children’s Heart Institute, 601 5th Street South, Saint Petersburg, Florida 33701, United States of America. Tel: +727 767 3333; Fax: +727 767 8900; E-mail: jamie.decker@jhmi.edu
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Abstract

Valvar heart disease can be complicated by hemodynamic derangements, depending on the degree of the abnormality. Stenosis causes pressure overload of the chamber draining through the valve and regurgitation results in volume overload. Many lesions have a component of both, resulting in both pressure and volume overload. Increased wall stress causes myocardial stretching and fibrosis, resulting in scarring; a nidus for arrhythmia development. Arrhythmias can complicate the clinical picture and increase the morbidity and mortality in patients with both congenital and acquired valvar disease. In adults with congenital heart disease, arrhythmias are the most common cause of sudden death, followed by heart failure. Valvar stenosis and insufficiency certainly contribute to this. This article highlights the need for arrhythmia surveillance for high-risk valvar lesions.

Keywords

Arrhythmiasvalvar heart diseasepediatrics
Type
Original Article
Information
Cardiology in the Young , Volume 24 , Issue 6: HeartWeek 2014 , December 2014 , pp. 1064 - 1070
Copyright
© Cambridge University Press 2014 

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Footnotes

*

Presented at All Children’s Hospital Johns Hopkins Medicine 14th International Symposium on Congenital Heart Disease, Saint Petersburg, Florida, 15–18 February 2014, Special Focus: Diseases of the Cardiac Valves from the Fetus to the Adult, Co-Sponsor: The American Association for Thoracic Surgery (AATS).

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