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Rare case of a superior sinus venosus atrial septal defect presenting with cyanosis

Part of: Cardiac Morphology Atrial Septal Defect (ASD)

Published online by Cambridge University Press:  05 April 2019

Maher Abadeer ,
Michael Luceri  and
Boban Abraham
Maher Abadeer
Affiliation:
Department of Pediatrics, St. Christopher’s Hospital for Children, Philadelphia, Pennsylvania, USA
Michael Luceri
Affiliation:
Department of Cardiology, Nemours Alfred I. duPont Hospital for Children, Wilmington, Delaware, USA
Boban Abraham*
Affiliation:
Department of Cardiology, St. Christopher’s Hospital for Children, Philadelphia, Pennsylvania, USA
*
Author for correspondence: Boban Abraham, MD, St. Christopher’s Hospital for Children, Department of Cardiology, 160 E Erie Ave, Philadelphia, PA 19134, USA. Tel: 215-427-4816; Email: bobanpabr@gmail.com
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Abstract

Cyanosis in a newborn is commonly due to intracardiac shunts or duct-dependent lesions. Systemic venous anomalies are uncommon and sinus venous atrial septal defects do not usually present with cyanosis. We report the case of a 4-month-old female with persistent hypoxemia due to a right superior vena cava overriding a superior sinus venous atrial septal defect resulting in a right to left shunt.

Keywords

Anomalous right superior vena cavasuperior sinus venosus defectcyanosis
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 4 , April 2019 , pp. 544 - 546
Copyright
© Cambridge University Press 2019 

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References

Hoey, ETD, Lewis, G, Yusuf, S. Multidector CT assessment of partial anomalous pulmonary venous return in association with sinus venosus type atrial septal defect. Quant Imaging Med Surg 2014; 4(5): 433–434.Google Scholar
Van Praagh, S, Geva, T, Lock, JE, et al. Biatrial or left atrial drainage of the right superior vena cava: anatomic, morphogenetic, and surgical considerations—report of three new cases and literature review. Pediatr Cardiol 2003; 24: 350–363.CrossRefGoogle ScholarPubMed
Vassallo, M, Pascotto, M, Pisacane, C, et al. Right superior vena cava draining into the left atrium: prenatal diagnosis and postnatal management. Ultrasound Obstet Gynecol 2006; 27: 445–448.CrossRefGoogle ScholarPubMed
Shapiro, EP, Al-Sadir, J, Campbell, NPS, et al. Drainage of right superior vena Cava into both atria. Circulation 1981; 63: 712–717.CrossRefGoogle ScholarPubMed
Truman, AT, Rao, PS, Kulangara, RJ. Use of contrast echocardiography in diagnosis of anomalous connection of right superior vena cava to left atrium. Br Heart J 1980; 44: 718–723.CrossRefGoogle ScholarPubMed
Sonavane, SK, Milner, DM, Singh, SP,, et al. Comprehensive imaging review of the superior vena cava. RadioGraphics 2015; 35(7): 1873–1892.CrossRefGoogle ScholarPubMed
Wong, TT, Lee, LS, Wang, HS, et al. Brain abcesses in children: a co-operative study of 83 cases. Child Nerv Syst 1989; 5: 19–24.CrossRefGoogle Scholar
Erol, I, Metin, IL, Alehan, F, et al. Brain abscess associated with isolated left superior vena cava draining into the left atrium in the absence of coronary sinus and atrial septal defect. Cardiovasc Intervent Radiol 2006; 29: 454–456.CrossRefGoogle ScholarPubMed
Ch’ng, JK, Soon, JL, Lim, CH. Paradoxical emboli from left superior vena cava causing recurrent brain abscess. Singapore Med J 2012; 53(1): e21–e23.Google ScholarPubMed
Menachem, JN, Sundaram, SN, Rhodes, JF. Recurrent cerebral abscess secondary to a persistent left superior vena cava. Congenit Heart Dis 2014; 9: E78–E84.CrossRefGoogle ScholarPubMed
Ling, Y, Gan, C, Sandeep, B, et al. Modified Warden procedure for partial anomalous pulmonary venous return to the superior vena cava. J Card Surg 2016; 31: 631–634.CrossRefGoogle Scholar
Narayen, IC, Blom, NA, Ewer, AK, et al. Aspects of pulse oximetry screening for critical congenital heart defects: when, how, and why? Arch Dis Child Fetal Neonatal Ed 2016; 101: F162–F167.CrossRefGoogle ScholarPubMed

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