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Clinical course of a fetus with hypoplastic left heart syndrome and premature ductal constriction

Part of: Hypoplastic Left Heart Syndrome (HLHS)

Published online by Cambridge University Press:  27 December 2018

Anita Krishnan ,
Lauren Tague ,
Harish Rudra ,
Subechhya Pradhan ,
Gilbert Vezina  and
Catherine Limperopoulos
Anita Krishnan*
Affiliation:
Division of Cardiology, Children’s National Medical Center, Washington, DC, USA
Lauren Tague
Affiliation:
Division of Cardiology, Children’s National Medical Center, Washington, DC, USA
Harish Rudra
Affiliation:
Department of Pediatrics, Fairfax Inova Hospital, Falls Church, VA, USA
Subechhya Pradhan
Affiliation:
Department of Radiology, Children’s National Medical Center, Washington, DC, USA
Gilbert Vezina
Affiliation:
Department of Radiology, Children’s National Medical Center, Washington, DC, USA
Catherine Limperopoulos
Affiliation:
Department of Radiology, Children’s National Medical Center, Washington, DC, USA
*
Author for correspondence: A. Krishnan, MD, Children’s National Medical Center, Department of Cardiology, 111 Michigan Avenue NW, Suite WW3-200, Washington, DC, 20010, USA. Tel: +(202) 476-2020; E-mail: akrishna@childrensnational.org
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Abstract

Premature ductal constriction was diagnosed in a 30-week gestation fetus with hypoplastic left heart syndrome. The fetus developed right ventricular hypertrophy and mild tricuspid regurgitation. Foetal neuroimaging showed slowed growth of the brain and increased lactate. We describe the imaging and clinical findings. Fetuses with critical CHD and in utero ductal constriction are at increased risk of morbidity and mortality, and require appropriate counselling.

Keywords

Hypoplastic left heartductus arteriosus
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 2 , February 2019 , pp. 216 - 218
Copyright
© Cambridge University Press 2018 

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Footnotes

Cite this article: Krishnan A, Tague L, Rudra H, Pradhan S, Vezina G, Limperopoulos C. (2018) Clinical course of a fetus with hypoplastic left heart syndrome and premature ductal constriction. Cardiology in the Young page 216 of 218. doi: 10.1017/S1047951118001701

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