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A familial variant of the Scimitar syndrome with a meandering pulmonary vein

Published online by Cambridge University Press:  26 May 2006

Ghassan H. Al-Naami  and
Riyadh M. Abu-Sulaiman
Ghassan H. Al-Naami
Affiliation:
Pediatric Cardiology Division, Cardiac Science Department, King AbdulAziz Medical City, Riyadh, Saudi Arabia
Riyadh M. Abu-Sulaiman
Affiliation:
Pediatric Cardiology Division, Cardiac Science Department, King AbdulAziz Medical City, Riyadh, Saudi Arabia
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Abstract

We report a rare variant of the Scimitar syndrome, in which the right lower pulmonary vein takes a meandering course before finally connecting in normal fashion to the left atrium. The pulmonary parenchymal segment drained by the tortuous vein is supplied by a systemic collateral artery, which was coiled via a catheter. We also closed the intracardiac defects by surgery. The elder brother of the patient had classical Scimitar syndrome.

Keywords

Congenital heart diseasevenous returnechocardiographyangiography
Type
Brief Report
Information
Cardiology in the Young , Volume 16 , Issue 3 , June 2006 , pp. 308 - 309
Copyright
© 2006 Cambridge University Press

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