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Myocardial infarct late after Fontan-type surgery in pulmonary atresia and intact ventricular septum: a must-know complication! About a case report

Part of: Cardiac Morphology Atrial Septal Defect (ASD) Echocardiography Interventional Cardiology

Published online by Cambridge University Press:  27 April 2021

Marie Wilkin Open the ORCID record for Marie Wilkin [Opens in a new window] ,
Jean Michel Rauzier  and
Caroline Ovaert
Marie Wilkin*
Affiliation:
Pediatric and Congenital Cardiology, Timone Hospital, Assistance Publique – Hôpitaux de Marseille, Marseille, France
Jean Michel Rauzier
Affiliation:
Pediatric Department, Nimes University Hospital, Nimes, France
Caroline Ovaert
Affiliation:
Pediatric and Congenital Cardiology, Timone Hospital, Assistance Publique – Hôpitaux de Marseille, Marseille, France Faculté des Sciences Médicales et Paramédicales, Ecole de Médecine, Aix Marseille University, Marseille, France
*
Author for correspondence: Marie Wilkin, Cardiologie Pédiatrique et congénitale, Timone Enfants (2ième étage) – AP-HM, 264 Rue Saint-Pierre, 13385 Marseille cedex 05, France. Fax: + 33 4 91 38 56 38. E-mail: marie-aude.wilkin@ap-hm.fr
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Abstract

Coronary abnormalities are frequent in pulmonary atresia and intact ventricular septum, mainly in patients with a very diminutive right ventricle. They severely impact on early and late prognosis. We describe an 8-year-old girl who presented with myocardial ischaemia, late after uneventful Fontan completion. The importance of precise delineation of the coronary anatomy upon initial assessment and during follow-up is emphasised.

Keywords

Pulmonary atresia with intact ventricular septumcoronary anomaliesischaemia
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 10 , October 2021 , pp. 1709 - 1711
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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