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Pulmonary atresia with intact ventricular septum in the setting of D-transposition of the great arteries associated with hypoplastic left ventricle and severe mitral regurgitation

Part of: Cardiac Morphology

Published online by Cambridge University Press:  28 February 2022

Kota Suzuki Open the ORCID record for Kota Suzuki [Opens in a new window] ,
Norie Mitsushita  and
Akio Ikai
Kota Suzuki*
Affiliation:
Department of Pediatrics, Yamagata University Hospital, Yamagata, Japan
Norie Mitsushita
Affiliation:
Department of Cardiology, Shizuoka Children’s Hospital, Shizuoka, Japan
Akio Ikai
Affiliation:
Department of Cardiac and Thoracic Surgery, Shizuoka Children’s Hospital, Shizuoka, Japan
*
Author for correspondence: K. Suzuki, MD, Department of Pediatrics, Yamagata University Hospital, 2-2-2, Iidanishi, Yamagata-City, Japan. Tel: +81-23-628-5329; Fax: +81-23-628-5332. E-mail: bellwood04411055@yahoo.co.jp
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Abstract

We report the first successful Glenn procedure for pulmonary atresia with intact ventricular septum in the setting of D-transposition of the great arteries. This case was complicated by hypoplastic left ventricle and severe mitral regurgitation. Partial closure of the mitral valve at the time of Blalock-Taussig shunting resulted in improvement of heart failure.

Keywords

D-transpositionpulmonary atresia with intact ventricular septumhypoplastic left ventricleendocardial fibroelastosismitral regurgitation
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 11 , November 2022 , pp. 1845 - 1847
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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References

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