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Severely obstructed totally anomalous pulmonary venous return with residual connection to the left atrium

Published online by Cambridge University Press:  18 June 2007

Lik Eng Loh ,
Katherine Brown  and
Jan Marek
Lik Eng Loh
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
Katherine Brown
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
Jan Marek*
Affiliation:
Cardiothoracic Unit, Great Ormond Street Hospital for Sick Children, London, United Kingdom
*
Correspondence to: Dr Jan Marek, MD, PhD, Director of Echocardiography, Consultant Paediatric Cardiologist, Great Ormond Street Hospital for Sick Children, Great Ormond Street, London WC1N 3JH, United Kingdom. Tel: +44 (0)207 405 9200, Ext 8012; Fax: +44 (0)207 813 8262; E-mail: MarekJ@gosh.nhs.uk
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Abstract

Totally anomalous pulmonary venous return may present diagnostic difficulty to clinicians, as it often appears similar to severe neonatal pulmonary disease. We describe a neonate who presented with severely obstructed pulmonary venous return, but with a residual venous connection to the left atrium. The unusual anatomy confounded the diagnosis. To our knowledge, this particular permutation has not previously been described. Our experience indicates that echocardiographic interrogation should be repeated in cases where there is no response to conventional therapy, and all individual pulmonary veins should be observed carefully.

Keywords

Echocardiographyextracorporeal membrane oxygenationcongenital heart disease
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 4 , August 2007 , pp. 441 - 444
Copyright
Copyright © Cambridge University Press 2007

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