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Otological findings in idiopathic hyperphosphatasia

Published online by Cambridge University Press:  29 June 2007

Levent Sennaroǧlu ,
Bulent Sozeri  and
Arzu Sungur
Levent Sennaroǧlu*
Affiliation:
Department of Otolaryngology Head and Neck Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Bulent Sozeri
Affiliation:
Department of Otolaryngology Head and Neck Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Arzu Sungur
Affiliation:
Department of Pathology, Hacettepe University Faculty of Medicine, Ankara, Turkey.
*
Address for correspondence: Levent Sennaroǧlu, M.D., Büklüm Sokak 45/16, Kavaklidere, Ankara 06660, Turkey Fax: 90-311-3113500 e-mail: lsennar@tr-net-net.tr.
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Abstract

A 17-year-old male patient was admitted because of progressive hearing loss since the age of six. His former blood and radiology investigation had revealed idiopathic hyperphosphatasia. On ENT examination bilateral thickened tympanic membranes with severe mixed-type hearing loss was diagnosed. Computerized tomography (CT) demonstrated expansion of the calvarial bones, including the temporal bones, except for the otic capsule. Middle-ear exploration revealed thickened middle-ear mucosa and a stone hard, immobile bony mass instead of the normal ossicular chain at the posterior superior part of the mesotympanum. No ossicular reconstruction could be attempted and the patient was rehabilitated with a hearing aid.

Keywords

Idiopathic hyperphosphatasiaHearing lossMiddle-ear surgery
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 2 , February 1999 , pp. 158 - 160
Copyright
Copyright © JLO (1984) Limited 1999

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References

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