Hostname: page-component-848d4c4894-nmvwc Total loading time: 0 Render date: 2024-06-29T02:14:55.989Z Has data issue: false hasContentIssue false
  • English
  • Français

Cochlear implantation in superficial siderosis

Published online by Cambridge University Press:  29 June 2007

Richard M. Irving  and
John M. Graham
Richard M. Irving*
Affiliation:
Ferens Cochlear Implant Centre, The Royal Ear Hospital, London, UK.
John M. Graham
Affiliation:
Ferens Cochlear Implant Centre, The Royal Ear Hospital, London, UK.
*
Address for correspondence: Mr Richard M. Irving, M.D., F.R.C.S., Deparment of Otolaryngology – Head and Neck Surgery, University of California, San Francisco, 350 Parnassus Avenue, Suite 210, San Francisco, California 94117, U.S.A. Fax: 00 1 415 476 0666
Get access Rights & Permissions [Opens in a new window]

Abstract

Superficial siderosis is a rare central nervous system disorder characterized by deafness, ataxia, and pyramidal signs. The hearing loss is believed to be predominantly neural and is usuallly progressive and bilateral. Careful assessment is therefore necessary to determine the best approach to hearing rehabilitation. A case is presented of usperficial siderosis in a young woman who has benegited significantly from cochlear implantation using the Nucleus dvice.

Keywords

SiderosisHearing loss, sensorineuralCochlear implant
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 12 , December 1996 , pp. 1151 - 1153
Copyright
Copyright © JLO (1984) Limited 1996

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Footnotes

Presented at IIIrd Paris International Congress on Cochlear Implants April, 1995

References

Fearnley, J. M., Stevens, J. M., Rudge, P. (1995) Superficial siderosis of the central nervous system. Brain 118: 1051–1066.CrossRefGoogle ScholarPubMed
Fishman, R. A. (1993) Superficial siderosis. Annals of Neurology 34: 635–636.CrossRefGoogle ScholarPubMed
Koeppen, A. H., Dentinger, M. P. (1988) Brain haemosiderin and superficial siderosis of the central nervous system. Journal of Neuropathology and Experimental Neurology 47: 249–270.CrossRefGoogle ScholarPubMed
Koeppen, A. H., Dickson, A. C., Chu, R. C., Thach, R. E. (1993) The pathogenesis of superficial iderosis of the central nervous system. Annals of Neurology 34: 646–653.CrossRefGoogle ScholarPubMed
Kott, E., Bechar, M., Bornstein, B., Askenasy, H. M., Sandbank, U. (1966) Superficial haemosiderosis of the central nervous system. Acta Neurochirugica 14: 287–298.CrossRefGoogle ScholarPubMed
Neuman, M. A. (1948) Hemochromotosis of the central nervous system. Journal of Neuropathology and Experimental Neurology 7: 19–34.CrossRefGoogle Scholar
Neuman, M. A. (1956) Hemochromatic pigmentation of the central nervous system. Archives of Neurology and Psychiatry 76: 355–368.CrossRefGoogle Scholar
Pribitkin, E. A., Rondinella, L., Rosenberg, S. I., Yousem, D. M. (1994) Superficial siderosis of the central nervous system: An underdiagnosed cause of sensorineural hearing loss and ataxia. American Journal of Otology 15: 415–418.Google ScholarPubMed
Revesz, T., Earl, C. T., Barnard, R. O. (1988) Superficial siderosis of the central nervous system presenting with longstanding deafness. Journal of the Royal Society of Medicine 81: 479–481.CrossRefGoogle ScholarPubMed
Sadeh, M., Sandbach, U. (1980) Neuraxonal dystrophy and hemosiderin in the central nervous system. Annals of Neurology 7: 286–287.CrossRefGoogle Scholar
Stevens, I., Peterson, D., Grodd, W., Poremba, M., Dichgans, J. (1991) Superficial siderosis of the central nervous system. A 37 follow up of a case and review of the literature. European Archives of Psychiatry and Clinical Neurosciences 241: 57–60.CrossRefGoogle ScholarPubMed
Tomlinson, B. E., Walton, J. N. (1964) Superficial haemosiderosis of the central nervous system. Journal of Neurology, Neurosurgery and Psychiatry 27: 332–339.CrossRefGoogle ScholarPubMed