Skip to main content Accessibility help

We use cookies to distinguish you from other users and to provide you with a better experience on our websites. Close this message to accept cookies or find out how to manage your cookie settings.

Close cookie message
×
Hostname: page-component-848d4c4894-ndmmz Total loading time: 0 Render date: 2024-06-02T11:11:21.733Z Has data issue: false hasContentIssue false

Case 8 - Williams-Campbell syndrome

Published online by Cambridge University Press:  07 October 2011

By
Thomas Hartman
Edited by
Thomas Hartman
Thomas Hartman
Affiliation:
Mayo Clinic, Rochester
Get access

Summary

Imaging

Williams-Campbell syndrome is characterized by cystic bronchiectasis in the fourth to sixth order bronchi [1, 2] (Figure 8.1–8.3). If expiratory images are obtained, collapse of the bronchiectatic segments can be seen [1–3]. Hyperinflation or emphysematous changes may also be seen in the lung distal to the bronchiectatic regions. The cause of the bronchiectasis is due to defective or absent cartilage in the walls of the fourth to sixth order bronchi.

Importance

Williams-Campbell syndrome has been postulated to be a congenital abnormality. At least two separate reports have shown a familial occurrence [3]. Therefore, recognition of this abnormality in a patient should lead to additional investigations of family members.

Type
Chapter
Information
Pearls and Pitfalls in Thoracic Imaging
Variants and Other Difficult Diagnoses
 , pp. 20 - 21
Publisher: Cambridge University Press
Print publication year: 2011

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Watanabe, YNishiyama, HKanayama, HCase report: congenital bronchiectasis due to cartilage deficiency: CT demonstrationJ Comput Assist Tomogr 1987 11 701CrossRefGoogle ScholarPubMed
Kaneko, KKudo, STashiro, MCase report: computed tomography findings in Williams-Campbell syndromeJ Thorac Imaging 1991 6 11CrossRefGoogle ScholarPubMed
Palmer, SMLayish, DTKussin, PSLung transplantation for Williams-Campbell syndromeChest 1998 113 534CrossRefGoogle ScholarPubMed

Save book to Kindle

To save this book to your Kindle, first ensure coreplatform@cambridge.org is added to your Approved Personal Document E-mail List under your Personal Document Settings on the Manage Your Content and Devices page of your Amazon account. Then enter the ‘name’ part of your Kindle email address below. Find out more about saving to your Kindle.

Note you can select to save to either the @free.kindle.com or @kindle.com variations. ‘@free.kindle.com’ emails are free but can only be saved to your device when it is connected to wi-fi. ‘@kindle.com’ emails can be delivered even when you are not connected to wi-fi, but note that service fees apply.

Find out more about the Kindle Personal Document Service.

Available formats
×

Save book to Dropbox

To save content items to your account, please confirm that you agree to abide by our usage policies. If this is the first time you use this feature, you will be asked to authorise Cambridge Core to connect with your account. Find out more about saving content to Dropbox.

Available formats
×

Save book to Google Drive

To save content items to your account, please confirm that you agree to abide by our usage policies. If this is the first time you use this feature, you will be asked to authorise Cambridge Core to connect with your account. Find out more about saving content to Google Drive.

Available formats
×