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Fatal neonatal hypertrophic cardiomyopathy with severe stenosis of the right ventricular outflow tract: echocardiographic diagnosis and potential therapy

Published online by Cambridge University Press:  19 August 2008

Tomomi Orino ,
Tadahiko Ito  and
Goro Takada
Tomomi Orino
Affiliation:
Department of Pediatrics, Akita University School of Medicine, Akita, Japan
Tadahiko Ito*
Affiliation:
Department of Pediatrics, Akita University School of Medicine, Akita, Japan
Goro Takada
Affiliation:
Department of Pediatrics, Akita University School of Medicine, Akita, Japan
*
Tadahiko Ito, MD, Department of Pediatrics, Akita University School of Medicine, 1-1-1 Hondo, Akita, Japan. Tel: 81-188-34-1111; Fax: 81-188-36-2620
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Abstract

We discuss the clinical course of aneonate with idiopathic hypertrophic cardiomyopathy who showed rapid progression of stenosis of the right ventricular outflow tract and reduction in size of the right ventricular cavity due to thicken ing of the ventricular septum. Medical treatment proved unsuccessful. We suggest that balloon atrial septostomy combined with construction of a Blalock-Taussig shunt may be effective in view of the hemodynamics, which mimic pulmonary atresia with intact interventricular septum.

Keywords

Idiopathic hypertrophic cardiomyopathyechocardiographyjright ventricular outflow tract stenosisneonate
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 1 , January 1999 , pp. 63 - 64
Copyright
Copyright © Cambridge University Press 1999

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References

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