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Isolated obstruction of the right ventricular infundibulum in a patient with Williams' syndrome

Published online by Cambridge University Press:  22 December 2006

Victor E. Grech ,
Robert Xuereb  and
Joseph V. DeGiovanni
Victor E. Grech
Affiliation:
Department of Paediatrics, St. Luke's Hospital, Guardamangia, Malta
Robert Xuereb
Affiliation:
Department of Cardiology, St. Luke's Hospital, Guardamangia, Malta
Joseph V. DeGiovanni
Affiliation:
Department of Cardiology, Birmingham Children's Hospital, Birmingham, United Kingdom
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Abstract

Williams' syndrome is a rare condition that is associated with severe cardiovascular manifestations. We report a patient with Williams' syndrome who also has isolated obstruction of the right ventricular infundibulum, an association that, to the best of our knowledge, has not been previously reported.

Keywords

Heart defectscongenitalright ventricular outflow obstruction
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 1 , February 2007 , pp. 105 - 106
Copyright
2007 Cambridge University Press

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