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Paroxysmal complete atrioventricular block in a patient with pulmonary atresia and intact ventricular septum

Published online by Cambridge University Press:  13 October 2010

Akash R. Patel ,
David Goldberg  and
Maully Shah
Akash R. Patel*
Affiliation:
Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, Pennsylvania, United States of America
David Goldberg
Affiliation:
Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, Pennsylvania, United States of America
Maully Shah
Affiliation:
Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, Pennsylvania, United States of America
*
Correspondence to: Dr A. R. Patel, MD, Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, 34th Street and Civic Center Blvd, Philadelphia, Pennsylvania 19104, United States of America. Tel: 215 590 2230; Fax: 215 590 5825; E-mail: patela@email.chop.edu
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Abstract

Sudden death in pulmonary atresia and intact ventricular septum with right ventricular dependent coronary circulation is a well-established complication, and is thought to be caused by myocardial ischaemia. We report a case of paroxysmal complete atrioventricular block that raises the possibility of an additional mechanism of sudden death.

Keywords

External cardiac ambulatory telemetrycongenital cardiac diseaseFontan procedure
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 1 , February 2011 , pp. 94 - 96
Copyright
Copyright © Cambridge University Press 2010

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