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Ruptured aneurysm of the right coronary sinus of Valsalva in a child with Down syndrome

Published online by Cambridge University Press:  18 April 2013

Najim Lahrouchi ,
Lukas A. J. Rammeloo ,
David R. Koolbergen  and
Jaroslav Hruda
Najim Lahrouchi
Affiliation:
Department of Pediatric Cardiology, VU University Medical Center, Amsterdam, The Netherlands
Lukas A. J. Rammeloo
Affiliation:
Department of Pediatric Cardiology, VU University Medical Center, Amsterdam, The Netherlands
David R. Koolbergen
Affiliation:
Department of Cardiothoracic Surgery, Leiden University Medical Center, Leiden, The Netherlands
Jaroslav Hruda*
Affiliation:
Department of Pediatric Cardiology, VU University Medical Center, Amsterdam, The Netherlands
*
Correspondence to: Dr J. Hruda, MD, PhD, Department of Pediatric Cardiology, VU University Medical Center, P.O. Box 7057, 1007 MB Amsterdam, The Netherlands. Tel: +31 20 444 2484; Fax: +31 20 444 2422; E-mail: j.hruda@vumc.nl
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Abstract

Aneurysms of one of the aortic sinuses of Valsalva are rare congenital or acquired lesions. Here we present the case of an adolescent with Down syndrome with ruptured aneurysm of the right coronary sinus into the right atrium. All sinuses of Valsalva were normal during cardiological screening owing to Down syndrome at the age of 2 weeks. Paediatricians should have a low threshold for referring patients with Down syndrome for cardiac re-evaluation because of the new onset of cardiac symptoms or cardiac physical findings, even in the situation in which there are normal echocardiographic findings in the past.

Keywords

Down syndromeaneurysmsinus of Valsalva
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 2 , April 2014 , pp. 376 - 378
Copyright
Copyright © Cambridge University Press 2013 

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