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The syndrome of pericarditis, arthritis, and camptodactyly: an under-recognized cause of pericardial constriction in children?

Published online by Cambridge University Press:  19 August 2008

Alfonso Buendía ,
Fause Attié  and
Manuel Martínez-Lavin
Alfonso Buendía
Affiliation:
Institute National de Cardiologia Ignatio Chavez, Mexico
Fause Attié
Affiliation:
Institute National de Cardiologia Ignatio Chavez, Mexico
Manuel Martínez-Lavin*
Affiliation:
Institute National de Cardiologia Ignatio Chavez, Mexico
*
Manuel Martínez-Lavín MD, Instituto Nacional de Cardiología Ignacio Chávez, Juan Badiano #1, 14080 Mexico D.F., Mexico. Tel: (525)5732911 exc. 175; Fax: (525)5730994; E-mail: mmlavin@infosel.net.mx
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Abstract

The syndrome encompassing the combination of pericarditis, arthritis, and camptodactyly is a rarely described cause of pericardial constriction in children. It is likely that this association is being under-recognized. We report a new case in which the skeletal abnormalities were subtle. The syndrome should be included in the differential diagnosis of any child with persistent non-inflammatory pericardial effusion. A careful search at the bedside for the associated skeletal abnormalities should lead to the correct diagnosis. Pericardiectomy is the treatment of choice.

Keywords

Constrictive pericarditiscamptodactylyarthritisfibrosis
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 5 , September 1999 , pp. 526 - 528
Copyright
Copyright © Cambridge University Press 1999

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References

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