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Unilateral interruption of pulmonary artery with pulmonary hypertension: a case for heart lung transplantation?

Part of: Cardiac Morphology

Published online by Cambridge University Press:  30 April 2019

Roopesh Singhal
Roopesh Singhal*
Affiliation:
Department of Cardiology, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India
*
Author for correspondence: R. Singhal, Department of Cardiology, U. N. Mehta Institute of Cardiology and Research Center, Civil Hospital Campus, Asarwa, Ahmedabad, Gujarat, India. Tel: +91-9099016535; Fax: +91-79-22682092; E-mail: roopeshrsinghal@gmail.com
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Abstract

Unilateral interruption of pulmonary artery is a rare congenital anomaly which is usually associated with other congenital heart disease. Even more rarely it may occur in isolation. Most of the cases are incidentally detected in adulthood. Some cases develop pulmonary hypertension for yet unknown reasons; such cases usually present in infancy with right heart failure. Surgical correction in such cases is associated with adverse outcomes. Heart lung transplantation should be considered in such patients. We report a 3-year-old boy with interruption of right pulmonary artery with severe pulmonary hypertension and right heart failure who was considered for heart lung transplantation.

Keywords

Interruption of pulmonary arteryunilateral absence of pulmonary arteryheart lung transplantationpulmonary hypertensionright heart failure
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 5 , May 2019 , pp. 704 - 707
Copyright
© Cambridge University Press 2019 

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