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Fibromuscular dysplasia of the coronary arteries: a rare cause of death in infants and young children

Published online by Cambridge University Press:  14 May 2015

Carolin Mogler ,
Wolfgang Springer  and
Matthias Gorenflo
Carolin Mogler*
Affiliation:
Institute of Pathology, University Hospital Heidelberg, Germany
Wolfgang Springer
Affiliation:
Department of Pediatric Cardiology, University Hospital Heidelberg, Germany
Matthias Gorenflo
Affiliation:
Department of Pediatric Cardiology, University Hospital Heidelberg, Germany
*
Correspondence to: Dr C. Mogler, Institute of Pathology, Im Neuenheimer Feld 224, 69120 Heidelberg, Germany. Tel: +496 221 563 8175; Fax: +49 622 156 5251; E-mail: Carolin.Mogler@med.uni-heidelberg.de
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Abstract

Fibromuscular dysplasia is a common vascular disease, which mainly affects the renal arteries. In this study, we report the case of a 1-day-old infant who presented with severe left ventricular dysfunction immediately after birth, and subsequently died 3 days postnatally. At autopsy, an extensive myocardial infarction of the left ventricle and the septum was found, caused by an isolated fibromuscular dysplasia of left coronary artery.

Keywords

Fibromuscular dysplasiacoronary arterymyocardial infarctioncause of death in infants
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Issue 1 , January 2016 , pp. 202 - 205
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Copyright
© Cambridge University Press 2015 

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