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Diagnostic and treatment challenges in neurofibroma concerning the external nose

Published online by Cambridge University Press:  15 December 2021

N Shakrawal Open the ORCID record for N Shakrawal [Opens in a new window] ,
M Chouhan  and
B Solanki
N Shakrawal*
Affiliation:
Department of Otorhinolaryngology and Head–Neck Surgery, Dr Sampurnanand Medical College, Jodhpur, India
M Chouhan
Affiliation:
Department of Otorhinolaryngology and Head–Neck Surgery, Dr Sampurnanand Medical College, Jodhpur, India
B Solanki
Affiliation:
Department of Otorhinolaryngology and Head–Neck Surgery, Dr Sampurnanand Medical College, Jodhpur, India
*
Author for correspondence: Dr Neha Shakrawal, Department of Otorhinolaryngology and Head–Neck Surgery, Dr Sampurnanand Medical College, Jodhpur, Rajasthan, India342005 Fax: +91 291 274 0531 E-mail: drnehasnmc@gmail.com
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Abstract

Background

This paper discusses clinical features and management aspects of an extremely rare entity, neurofibroma of the external nose.

Methods

Database searches were performed using PubMed, Embase and Google Scholar to identify previously published articles.

Results

Twelve articles comprising 13 patients with neurofibroma of the external nose were included. The mean age of presentation was 31 years. Sixty-nine per cent of patients were diagnosed at final histopathology. External approach rhinoplasty was performed in 76.9 per cent of patients, while the intranasal approach was used in 15.3 per cent of patients. There was a 15.3 per cent association with neurofibromatosis type 1. Recurrence was noted in 23 per cent of patients.

Conclusion

It may be challenging to diagnose this entity clinically because of its rarity and striking features on histopathology. Neurofibroma of the external nose should be kept in mind as a differential diagnosis for any soft progressive swelling over the nose. Management requires complete excision, with cosmesis and restoration of functions.

Keywords

NeurofibromaExternal NoseNeurofibromatosisNeurofibromatosis Type 1
Type
Review Article
Information
The Journal of Laryngology & Otology , Volume 136 , Issue 6 , June 2022 , pp. 473 - 478
Copyright
Copyright © The Author(s), 2021. Published by Cambridge University Press on behalf of J.L.O. (1984) LIMITED

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Footnotes

Dr N Shakrawal takes responsibility for the integrity of the content of the paper

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