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Hearing loss associated with large internal auditory meatus: a report of five paediatric cases

Published online by Cambridge University Press:  29 June 2007

Catherine S. Birman  and
William P. R. Gibson
Catherine S. Birman*
Affiliation:
New Children's Hospital, Royal Alexandra Hospital for ChildrenSydney, Australia.
William P. R. Gibson
Affiliation:
Department of Surgery, University of Sydney, Sydney, Australia.
*
Address for correspondence: Dr Catherine Birman, 39 Palmerston Road, Hornsby NSW 2077, Australia. Fax: +612 9482 2036.
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Abstract

This paper describes the abnormality of a large internal auditory meatus (LIAM). Computed tomography (CT) scans show the otic capsule to be affected by a widened, bulbar internal auditory meatus with loss of or reduction of the bony wall dividing the lateral fundus of the meatus from the cochlea. The vestibule is abnormally dilated. We report five cases of children with LIAM and profound hearing loss. Three of these children are girls and two children were boys. Three had congenital progressive hearing loss, one of these had an accompanying large vestibular aqueduct and dysplasia of the cochlea. Two patients had had meningitis resulting in profound loss.

Keywords

Hearing loss, sensorineural, aetiologyChildInfantTemporal boneTomography, X-ray computed
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 11 , November 1999 , pp. 1015 - 1019
Copyright
Copyright © JLO (1984) Limited 1999

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References

Anderson, C. (1985) The empty internal auditory canal. Australasian Radiology 29: 116–121.CrossRefGoogle ScholarPubMed
Aoki, S., Barkovich, A. J., Nishimura, K., Kjos, B. O., Machida, T., Cogen, P., Edwards, M., Norman, D. (1989) Neurofibromatosis Type 1 and 2: Cranial CR findings. Radiology 172(2): 527–534.CrossRefGoogle Scholar
Beaumont, D., Whyte, A. (1994) Radiology of the temporal bone. Australian Journal of Otolaryngology 1: 513–526.Google Scholar
Crain, M., Dolan, K. (1990) Internal auditory canal enlargement in Paget's disease appearing as bilateral acoustic neuromas. Annals of Otology, Rhinology and Laryngology 99: 833–834.CrossRefGoogle ScholarPubMed
Gibson, W. P. R. (1997) Cochlear implant in children. Chapter 11. In Scott-Brown's Otolaryngology. 6th Edition. (Kerr, A., ed.). Butterworths. pp 1–20.Google Scholar
Kitamura, K., Senba, T., Komatsuzaki, A. (1989) Bilateral internal auditory canal enlargement without acoustic nerve tumour in von Recklinghausen neurofibromatosis. Neurofibromatosis 2: 47–52.Google ScholarPubMed
Phelps, P. D., Reardon, W., Pembrey, M., Bellman, S., Luxon, L. (1991) X-linked deafness, stapes gusher and a distinctive defect of the inner ear. Neuroradiology 33: 326–330.CrossRefGoogle Scholar
Sakashita, T., Sando, I. (1996) Postnatal development of the internal auditory canal studied by computer-aided three-dimensional reconstruction and measurement. Annals of Otology, Rhinology and Laryngology 104: 469–475.CrossRefGoogle Scholar
Schachern, P., Paparella, M., Hybertson, R., Sano, S., Duvall, A. (1992) Bacterial tympanogenic labyrinthitis, meningitis, and sensorineural damage. Archives of Otolaryngology – Head and Neck Surgery 118: 53–57.CrossRefGoogle ScholarPubMed
Tomura, N., Sashi, R., Kobayashi, M., Hirano, H., Hashimoto, M., Watari, J. (1995) Normal variations of the temporal bone on high resolution CT: their incidence and clinical significance. Clinical Radiology 50: 144–148.CrossRefGoogle ScholarPubMed
Valvassori, G. (1995) The internal auditory canal revisited. The high-definition approach. Otolaryngologic Clinics of North AMerica 28: pp 431–451.CrossRefGoogle ScholarPubMed
Vovyodic, F., Whyte, A., Beaumont, G. D. (1996) Bilateral internal auditory canal enlargement in the absence of intra canalicular tumour. Australian Journal of Otolaryngology 2: 437–439.Google Scholar
Weinberg, P., Kim, K., Gore, R. (1981) Unilateral enlargement of the internal auditory canal: a developmental variant. Surgical Neurotology 15: 39–42.CrossRefGoogle ScholarPubMed
Wilson, J. T., Leivy, S. W., Sofferman, R. A., Wald, S. L. (1990/1991) Mondini dysplasia: spontaneous cerebrospinal fluid otorrhea. New perspectives in management. Pediatric Neurosurgery 16: 260–264.CrossRefGoogle ScholarPubMed