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Meatoplasty in Marfan syndrome

Published online by Cambridge University Press:  29 June 2007

J. E. Fenton  and
P. A. Fagan
J. E. Fenton
Affiliation:
Otology Department, St. Vincent's and Scottish Hospitals, Sydney, Australia.
P. A. Fagan*
Affiliation:
Otology Department, St. Vincent's and Scottish Hospitals, Sydney, Australia.
*
Address for correspondence: Dr P. A. Fagan, 352 Victoria St., Darlinehurst, N.S.W., 2010, Australia, Fax: (02) 3605419
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Abstract

Marfan syndrome (MS) is a rare connective tissue disorder, uncommon in otological practice. Ear surgery in MS has not been previously reported. An identical complication of meatoplasty developed in two patients with MS after modified radical mastoidectomy and meatoplasty for chronic otitis media. Both cases presented postoperatively with an external auditory canal narrowing when the walls of the initial meatoplasty in both cases collapsed. It is proposed that this occurred because of the inherent structural abnormality of the cartilage in Marfan syndrome. A simple technique of revision meatoplasty is described that resulted in successful management of these cases.

Keywords

Ear cartilages, surgeryMarfan syndrome
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 5 , May 1996 , pp. 456 - 458
Copyright
Copyright © JLO (1984) Limited 1996

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