Book contents
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Case 44 Ruptured appendicitis mimicking an intussusception
- Case 45 Choledochal cyst
- Case 46 Henoch–Schönlein purpura
- Case 47 Biliary atresia
- Case 48 Mesenchymal hamartoma of the liver
- Case 49 Lymphoid follicular hyperplasia
- Case 50 Midgut volvulus
- Case 51 Foveolar hyperplasia: post prostaglandin therapy
- Case 52 Pneumatosis cystoides intestinalis
- Case 53 Desmoplastic small round cell tumor
- Case 54 Post-transplantation lymphoproliferative disorder
- Case 55 Traumatic pancreatic injury
- Case 56 Meconium ileus
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Case 48 - Mesenchymal hamartoma of the liver
from Section 5 - Gastrointestinal imaging
Published online by Cambridge University Press: 05 June 2014
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Case 44 Ruptured appendicitis mimicking an intussusception
- Case 45 Choledochal cyst
- Case 46 Henoch–Schönlein purpura
- Case 47 Biliary atresia
- Case 48 Mesenchymal hamartoma of the liver
- Case 49 Lymphoid follicular hyperplasia
- Case 50 Midgut volvulus
- Case 51 Foveolar hyperplasia: post prostaglandin therapy
- Case 52 Pneumatosis cystoides intestinalis
- Case 53 Desmoplastic small round cell tumor
- Case 54 Post-transplantation lymphoproliferative disorder
- Case 55 Traumatic pancreatic injury
- Case 56 Meconium ileus
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Summary
Imaging description
An infant who was several weeks old presented with an incidental finding of a palpable abdominal mass on a routine clinical examination. The child did not have fever or any other clinical abnormalities. The liver was palpable 10 cm below the right costal margin. Ultrasound and CT studies demonstrated a large, multiseptated cystic lesion in the right lobe of the liver (Fig. 48.1). This was thought to be most consistent with a mesenchymal cystic hamartoma of the liver.
Importance
Mesenchymal hamartoma is a rare, benign liver neoplasm, typically found in children less than two years of age. The lesion is slightly more common in boys than in girls. It is a developmental cystic liver tumor, composed of proliferations of variably myxomatous mesenchyme and malformed bile ducts. Treatment consists of surgical resection.
Typical clinical scenario
Patients typically present with an asymptomatic abdominal mass. Rarely, complications including ascites, jaundice, and even congestive heart failure can occur. Since mesenchymal hamartomas are congenital malformations, they may be detected prenatally. The size is highly variable. The lesions may grow rapidly in the postnatal period, followed by growth stasis or even some regression. Most lesions are located within the liver parenchyma, although rare cases of pedunculated lesions have been described as well.
- Type
- Chapter
- Information
- Pearls and Pitfalls in Pediatric ImagingVariants and Other Difficult Diagnoses, pp. 211 - 214Publisher: Cambridge University PressPrint publication year: 2014