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Chapter 50 - Marfan Syndrome in Pregnancy

from Section 8 - Connective Tissue Disorders in Pregnancy

Published online by Cambridge University Press:  23 February 2023

By
Marwa Salman
Edited by
Amira El-Messidi  and
Alan D. Cameron
Amira El-Messidi
Affiliation:
McGill University, Montréal
Alan D. Cameron
Affiliation:
University of Glasgow
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Summary

A 28-year-old nulligravida with Marfan syndrome is referred to your tertiary center’s high-risk obstetric unit for preconceptional counseling. She has no other medical issues.

Keywords

Marfan syndrome, pregnancyPreconception counselingGenetic riskPerinatal risks, complications, maternal-fetal morbidity, adverse outcomeInvestigationsCardiac surgery, indicationsContraindications, pregnancyAntepartum, intrapartum, postpartum managementAortic dissection, pregnancy
Type
Chapter
Information
OSCEs in Obstetrics and Maternal-Fetal Medicine
An Evidence-Based Approach
 , pp. 635 - 642
Publisher: Cambridge University Press
Print publication year: 2023

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References

Suggested Readings

Boodhwani, M, Andelfinger, G, Leipsic, J, et al. Canadian Cardiovascular Society position statement on the management of thoracic aortic disease. Can J Cardiol. 2014;30(6):577–589.CrossRefGoogle Scholar
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Goland, S, Elkayam, U. Pregnancy and Marfan syndrome. Ann Cardiothoracic Surg 2017; 6: 642–653.Google Scholar
Hiratzka, LF, Bakris, GL, Beckman, JA, et al. 2010 ACCF/AHA/AATS/ACR/ASA/SCA/SCAI/SIR/STS/SVM Guidelines for the diagnosis and management of patients with thoracic aortic disease: Executive summary: A report of the American College of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines, American Association for Thoracic Surgery, American College of Radiology, American Stroke Association, Society of Cardiovascular Anesthesiologists, Society for Cardiovascular Angiography and Interventions, Society of Interventional Radiology, Society of Thoracic Surgeons, and Society for Vascular Medicine. Anesth Analg. 2010;111(2):279–315.CrossRefGoogle Scholar
Lim, JCE, Cauldwell, M, Patel, RR, et al. Management of Marfan syndrome during pregnancy: a real world experience from a Joint Cardiac Obstetric Service. Int J Cardiol. 2017; 243:180–184.CrossRefGoogle ScholarPubMed
Monteiro, R, Salman, M, Montiero, S, et al. (eds.). Aortic dissection. Chapter 96 in Analgesia, Anaesthesia and Pregnancy. Cambridge: Cambridge University Press; 2019.CrossRefGoogle Scholar
Naud, K, Horne, G, Van den Hof, M. A woman with Marfan syndrome in pregnancy: managing high vascular risk with multidisciplinary care. J Obstet Gynaecol Can. 2015; 37(8):724–727.CrossRefGoogle ScholarPubMed
Prendes, C, Mani, K. Pregnancy and aortic dissection. Eur J Vas Endovas Surg; in press.Google Scholar
Regitz-Zagrosek, V, Roos-Hesselink, JW, Bauersachs, J, et al. 2018 ESC Guidelines for the management of cardiovascular diseases during pregnancy. Eur Heart J. 2018; 39(34):3165–3241.CrossRefGoogle ScholarPubMed
van Hagen, IM, Roos-Hesselink, JW. Aorta pathology and pregnancy. Best Pract Res Clin Obstet Gynaecol. 2014; 28(4):537–550.CrossRefGoogle ScholarPubMed

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